Familial idiopathic basal ganglia calcification: a challenging clinical–pathological correlation

Familial idiopathic basal ganglia calcification (Fahr’s disease)

Familial idiopathic basal ganglia calcification (Fahr`s disease) is a rare neurodegenerative disorder characterized by symmetrical and bilateral calcification of the basal ganglia. Calcifications may also occur in other brain regions such as dentate nucleus, thalamus, and cerebral cortex. Both familial and non-familial cases of Fahr`s disease have been reported, predominantly with autosomal-dom...

Idiopathic familial basal ganglia calcification associated with juvenile hypertension.

fahr disease: idiopathic basal ganglia calcification

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Basal ganglia calcification in idiopathic hypoparathyroidism

ABSTRACT: Hypoparathyroidism refers to a group of disorders in which extracellular calcium levels cannot be maintained within the normal range due to relative or absolute deficiency of parathyroid hormone. Clinically, hypoparathyroidism manifests predominantly as neuromuscular dysfunction caused by hypocalcemia. Basal ganglia calcification in particular is associated with hypoparathyroidism. Tw...

Fahr disease: Idiopathic basal ganglia calcification